{"id":280607,"date":"2025-02-09T08:09:18","date_gmt":"2025-02-09T12:09:18","guid":{"rendered":"https:\/\/www.eldiario.net\/portal\/?p=280607"},"modified":"2025-02-09T08:09:18","modified_gmt":"2025-02-09T12:09:18","slug":"que-es-la-progeria","status":"publish","type":"post","link":"https:\/\/www.eldiario.net\/portal\/2025\/02\/09\/que-es-la-progeria\/","title":{"rendered":"\u00bfQU\u00c9 ES LA PROGERIA?"},"content":{"rendered":"<p>Lic.Lupe Fern\u00e1ndez Calix &#8211; Enfermera U.M.S.A.<\/p>\n<p>Es una enfermedad rara gen\u00e9tica que provoca la aceleraci\u00f3n de la vejez en ni\u00f1os es altamente mortal al nacer presentan un peso y talla normal a los 10 a 12 meses se observa anomal\u00edas en el crecimiento llegan a pesar hasta 25 Kg una altura de 1<em>25<\/em> ms esta enfermedad es mortal y no tiene cura solo viven hasta la adolescencia 15 a\u00f1os algunos llegan a vivir hasta los 20 a\u00f1os un ni\u00f1o con esta patolog\u00eda tiene una inteligencia normal r\u00ede juega de acuerdo a su edad.<\/p>\n<p>Se caracteriza est\u00e1 patolog\u00eda por el endurecimiento de las arterias del coraz\u00f3n y cerebro denominadas arterioesclerosis qu\u00e9 limitan el flujo sangu\u00edneo provocando enfermedades Cardiovascular, Cerebrovascular, Hipertensi\u00f3n arterial, etc. lo que provoca decesos en ni\u00f1os que solo alcanzan a veces hasta la adolescencia sufren tambi\u00e9n dolores frecuentes generalizado por la vejez prematura.<\/p>\n<p>Causada por la alteraci\u00f3n en la prote\u00edna de la l\u00e1mina A componente principal que mantiene el n\u00facleo est\u00e1 L\u00e1mina A sufre una mutaci\u00f3n de un gen de la L\u00e1mina A llamada Progerina llamada tambi\u00e9n enfermedad de Hutchinson- Gilford.<\/p>\n<p><strong>\u00bfSIGNOS Y S\u00cdNTOMAS?<\/strong><\/p>\n<p>Dificultad en el crecimiento Desproporci\u00f3n cr\u00e1neo facial<\/p>\n<p>Perdida de cabello (alopecia)<\/p>\n<p>Perdida de la audici\u00f3n (o\u00eddo) y vista paulatinamente.<\/p>\n<p>Ojos prominentes<\/p>\n<p>Nariz en forma de pico<\/p>\n<p>Mand\u00edbula ment\u00f3n, boca peque\u00f1a y labios finos<\/p>\n<p>Endurecimiento de la piel y tirantes<\/p>\n<p>Perdida del tejido adiposo (grasa abdominal y piel)<\/p>\n<p>Piel manchada arrugada<\/p>\n<p>Venas visibles<\/p>\n<p>Envejecimiento prematuro<\/p>\n<p>Retraso en la formaci\u00f3n de dientes<\/p>\n<p>Cadera desplaza o llamada dislocaci\u00f3n de cadera<\/p>\n<p>Enfermedades del corazon cardiovascular<\/p>\n<p><strong>\u00bfQU\u00c9 DEBEMOS HACER?<\/strong><\/p>\n<p>Dieta saludable<\/p>\n<p>Acudir de inmediato a un Centro Hospitalario en caso de signos y s\u00edntomas para su tratamiento.<\/p>\n<p>Incentivar al control peri\u00f3dico de ni\u00f1o sano<\/p>\n<p>No a la automedicaci\u00f3n<\/p>\n<p>Proporcionar apoyo psicol\u00f3gico en el hogar<\/p>\n<p>Insertar a la sociedad con ni\u00f1os de su edad<\/p>\n<p>Por la importancia de esta enfermedad y casos de ni\u00f1os que padecen bullying en una sociedad carente de conocimiento de esta enfermedad para evitar y afectar la psicolog\u00eda del ni\u00f1o que sufre est\u00e1 patolog\u00eda se debe abordar este tema solo preservado la Salud de los ni\u00f1os afectados.<\/p>\n<p><strong>\u201cAPRECIA Y VALORA T\u00da SALUD TODOS LOS D\u00cdAS \u201c<\/strong><\/p>\n","protected":false},"excerpt":{"rendered":"<p>Lic.Lupe Fern\u00e1ndez Calix &#8211; Enfermera U.M.S.A. Es una enfermedad rara gen\u00e9tica que provoca la aceleraci\u00f3n de la vejez en ni\u00f1os es altamente mortal al nacer presentan un peso y talla normal a los 10 a 12 meses se observa anomal\u00edas en el crecimiento llegan a pesar hasta 25 Kg una altura de 125 ms esta [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":280608,"comment_status":"closed","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"_acf_changed":false,"footnotes":""},"categories":[52],"tags":[],"class_list":["post-280607","post","type-post","status-publish","format-standard","has-post-thumbnail","category-de-salud-mas-vida"],"acf":{"antetitulo":""},"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v28.5 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>\u00bfQU\u00c9 ES LA PROGERIA? - El Diario - Bolivia<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/www.eldiario.net\/portal\/2025\/02\/09\/que-es-la-progeria\/\" \/>\n<meta property=\"og:locale\" content=\"es_ES\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"\u00bfQU\u00c9 ES LA PROGERIA? - El Diario - Bolivia\" \/>\n<meta property=\"og:description\" content=\"Lic.Lupe Fern\u00e1ndez Calix &#8211; Enfermera U.M.S.A. 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